Primitive neuroectodermal tumor (PNET) of nasal cavity

This is case where an elderly woman referred to our clinic with history of recurrent epistaxis from right nostril for one year duration associated with persistent right nasal blockage, hyposmia, loss of weight and loss of appetite. On examination noted polypoidal mass at right sphenoethmoidal recess with evidence of previous surgery. Patient underwent endoscopic removal of the mass and histopathologic examination was reported as malignant small round blue cells tumors from right olfactory cleft and right ethmoidal air cells. Based on immunohistochemical examination, it was consistent with primitive neuroectodermal tumour (PNET).