Aggressive ovarian adenosarcoma with high grade sarcomatous and chondrosarcoma components in a young patient

Mullerian adenosarcoma (MA) was first defined as a special malignancy of uterine corpus in 1974. Although a few hundred cases were reported about uterine adenosarcomas, extrauterine adenosarcomas (EMA) are very rare. Thus, clinic and pathologic knowledge about extrauterine adenosarcomas are limited. This case report represents an ovarian mesodermal (mullerian) adenosarcoma, which contains dominantly high grade sarcomatous components along with chondrosarcoma components and very limited classical adenosarcoma areas in a 25 year-old female. To our knowledge, this is the first case report in the literature reporting the combination of features as diffuse presentation of sarcomatous overgrowth (SO) areas, scarcity of classical adenosarcoma areas, existence of chondrosarcoma areas in such a young patient.